Humoral Primary Immunodeficiencies

Humoral Primary Immunodeficiencies

D'Elios, Mario Milco; Rizzi, Marta

Springer International Publishing AG

01/2019

387

Dura

Inglês

9783319917849

15 a 20 dias

934


ebook

Descrição não disponível.
Preface.- 1. B cells and the B-cell immunological synapse.-2 Mucosal B cells.- 3 CVID. - 4 LOCID. - 5 Genetics of CVID. - 6 ICOS deficiency. - 7 CD19 deficiency.- 8 CD20 deficiency. - 9 CD21 deficiency. - 10 CD81 deficiency. - 11 TACI deficiency, . - 12 LRBA deficiency. - 13 BAFF receptor deficiency. - 14 TWEAK defects. - 15 NFKB2 deficiency. - 16 WHIM syndrome. - 17 Novel humoral PID genes. - 18 Class Switch Recombination defects,.- 19 Selective IgA deficiency.- 20 IgA with IgG subclass deficiency. - 21 Isolated IgG subclass deficiency. - 22 Thymoma with immunodeficiency. - 23 PRKC delta and PI3K-delta associated diseases. - 24 Differential diagnostic in hypogammaglobulinemia. - 25 Management of Humoral primary immunodeficiencies in pediatrics.- 26 Management of Humoral primary immunodeficiencies in adults.- 27 Vaccines in humoral PID.- 28 Humoral PID and neoplasias.- 29 Humoral PID and autoimmunity. - 30 Lung involvement.- 31 Gut involvement.- Subject Index.
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B-cell;Antibodies;Gammaglobulines;Common Variable Immune Deficiency;Clinical Phenotypes;PID genes;Autoimmunity;Infections;Lymphoma;Cancer;Tumor;infectious diseases